Congential Long QT syndrome
IDENTIFICATION : E-HOL-03-0480-013

In the mid eighties, Philippe Coumel initiated the systematic recording of Holter ECGs in patients with a prolonged ventricular repolarization.
This Holter database has been nurtured by Isabelle Denjoy, and after discovery of the underlying genetic basis of the syndrome phenotypic ECG data accumulated over 25 years have been linked with the results of genetic data obtained in LQTS patients (N=480).
This primary care-oriented database contains clinical data (demographics, symptomatic status, and beta-blocker treatment at the time of recording) of genotyped LQTS patients who have had one or repeated Holter ECG recording(s).

The distribution of types of LQTS patients in htis database is as follow:

	ECG files	Subjects
Jervell and Lange-Nielsen	39	24
LQT1	246	171
LQT2	145	89
LQT3	35	14
Others	15	9

 

Number of Leads: 2 or 3 lead Holter ECGs (in case of 2-lead ECGs, the third lead is zeroed)

->Beware ECG ID 387 have incorrect RR annotation file

->Beware ECG 177.ecg and 223.ecg are the same recording

Sampling Frequency : 200Hz

Amplitude Resolution: available in the ISHNE files

Total Clinical Information available for the database:

Subject

Filename

Gender

Symptoms

Therapy

Gene(s)

Mutation(s)

Age